Purpose:

Kimura’s disease is a rare, benign and chronic disease of unknown etiology. This pathology has 6-fold higher prevalence in males and has been initially referred to as eosinophilic hyperplastic lymphogranuloma; it is manifested by inflammatory thickening of subcutaneous tissue in the head and neck. In this case report, we aimed to share imaging findings of a patient with orbital involvement.

Materu0131al and Method:

The patient presented with swelling of the left upper eyelid and mild pain; the patient underwent orbital MRI with contrast enhancement and biopsy was performed. She (49-year-old, female) was re-admitted 7 months later due to similar swelling in the right eye and pain; and then underwent orbital MRI and assessments were carried out on these images.

Results:

The patient's white blood cell count was moderately high and, in contrast to the literature, eosinophil count was not markedly elevated. However, physical examination did not reveal any abnormality excluding mild pain which is in line with the literature. On the other hand, initial and control MR images have revealed inflammation of fat tissue and contrast uptake in the left anterosuperior preseptal area and in the right retroortibal space, respectively. Cross-sectional studies were consistent with orbital pseudotumor whereas extraocular muscle groups surrounded by extensive inflammatory fatty tissue were not affected and they were of normal calibration and signal intensity. Pathologic examination performed after the first admission of the patient was consistent with Kimura's disease by the appearance of vascular proliferation with eosinophylic infiltration.

Conclusion:

In this case report of a patient who was diagnosed with Kimura's disease that represents atypical clinical and radiological characteristics, we present rare features which, however, may raise the suspicion of this disease.

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