Cholangiocarcinoma is the cancer of the bile duct epithelium and usually presents with painless jaundice and weight loss. Cutaneous metastases have rarely been reported in cholangiocarcinoma. Most of the reports of cutaneous metastases of cholangiocarcinoma are those seen around the percutaneous biliary drainage in the abdominal skin due to implantation of tumor cells during the procedure. Here we report a 41-year old male patient who was diagnosed with cholangiocarcinoma The presented case is the first case of cholangiocarcinoma with distant cutaneous metastases to the face. Distant skin metastases of cholangiocarcinoma must be in the differential diagnosis if atypical cutaneous lesions appears in patients with known cholangiocarcinoma.

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